Complete ICD-10-CM coding and documentation guide for icd-10 coding for lipin-1 deficiency includes clinical validation requirements, medical necessity guidelines, and coding policies.
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Essential facts and insights about ICD-10 Coding for Lipin-1 Deficiency
Use ICD-10 code E88.81 for other specified metabolic disorders, ensuring proper documentation in clinical notes.
Additional codes that may be used with this diagnosis
Myoglobinuria
Use when myoglobinuria is present due to rhabdomyolysis.
The ICD-10 code for Lipin-1 deficiency is E88.81, which is used for other specified metabolic disorders.
Lipin-1 deficiency is diagnosed through genetic testing confirming LPIN1 mutations, often accompanied by recurrent rhabdomyolysis episodes.