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Home/Diagnosis/ICD-10 Coding for Waldenström Macroglobulinemia

ICD-10 Coding for Waldenström Macroglobulinemia

C88.0
C88.00
C88.01

Complete ICD-10-CM coding and documentation guide for icd-10 coding for waldenström macroglobulinemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Lymphoplasmacytic Lymphoma
WM
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Key Information: ICD-10 Coding for Waldenström Macroglobulinemia

Essential facts and insights about ICD-10 Coding for Waldenström Macroglobulinemia

Use ICD-10 code C88.0 for waldenström macroglobulinemia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Waldenström macroglobulinemia

Non-Billable
C88.0
Non-Billable

Diagnostic Criteria

clinical:
  • • Presence of MYD88 L265P mutation
coding:
  • • Use C88.00 for active disease, C88.01 for remission
documentation:
  • • Document bone marrow biopsy and serum IgM levels

Applicable To

  • • IgM monoclonal gammopathy
  • • ≥10% bone marrow lymphoplasmacytic infiltration

Important Notes

  • • Ensure remission status is documented and coded appropriately.

Waldenström macroglobulinemia not in remission

Billable Code
C88.00
Billable

Diagnostic Criteria

clinical:
  • • Hemoglobin <10 g/dL
  • • Platelets <100k/µL
  • • Constitutional symptoms

Applicable To

  • • Active disease with symptoms

Important Notes

  • • Ensure active disease status is clearly documented.

Waldenström macroglobulinemia in remission

Billable Code
C88.01
Billable

Diagnostic Criteria

clinical:
  • • Bone marrow biopsy confirmation
  • • IgM reduction by ≥50%

Applicable To

  • • Documented complete hematologic response

Important Notes

  • • Document remission status with supporting lab results.
Ancillary Codes

Additional codes that may be used with this diagnosis

R68.2

Hyperviscosity syndrome

Use if serum viscosity >5 cP or retinal hemorrhages are present.

G62.81

IgM-related neuropathy

Use for numbness/tingling in extremities with positive serum IgM.

Frequently Asked Questions

What is the ICD-10 code for Waldenström macroglobulinemia?

The ICD-10 code for Waldenström macroglobulinemia is C88.0, with specific codes C88.00 for not in remission and C88.01 for in remission.

How is Waldenström macroglobulinemia documented?

Documentation should include bone marrow biopsy results, serum IgM levels, and MYD88 mutation status to support diagnosis and coding.

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