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Home/Diagnosis/ICD-10 Coding for Waldenström's Macroglobulinemia

ICD-10 Coding for Waldenström's Macroglobulinemia

C88.00
C88.01

Complete ICD-10-CM coding and documentation guide for icd-10 coding for waldenström's macroglobulinemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
WMLymphoplasmacytic Lymphoma with IgM Production
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Key Information: ICD-10 Coding for Waldenström's Macroglobulinemia

Essential facts and insights about ICD-10 Coding for Waldenström's Macroglobulinemia

Use ICD-10 code C88.00 for waldenström's macroglobulinemia without complications, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Waldenström's macroglobulinemia without complications

Billable Code
C88.00
Billable

Diagnostic Criteria

  • • Bone marrow biopsy showing ≥10% lymphoplasmacytic infiltration
  • • MYD88 L265P mutation detected by PCR

Applicable To

  • • Asymptomatic Waldenström's macroglobulinemia

Important Notes

  • • Ensure documentation explicitly states Waldenström's macroglobulinemia.

Waldenström's macroglobulinemia with refractory/relapsed disease

Billable Code
C88.01
Billable

Diagnostic Criteria

  • • Progression after 2+ lines of therapy
  • • Documented resistance to treatments like ibrutinib

Applicable To

  • • Refractory Waldenström's macroglobulinemia

Important Notes

  • • Ensure documentation reflects treatment history and refractory status.
Ancillary Codes

Additional codes that may be used with this diagnosis

R70.1

Hyperviscosity syndrome

Use when hyperviscosity symptoms are present with WM.

Frequently Asked Questions

What is the ICD-10 code for Waldenström's macroglobulinemia?

The ICD-10 code for Waldenström's macroglobulinemia is C88.00 for cases without complications and C88.01 for refractory or relapsed disease.

How is Waldenström's macroglobulinemia diagnosed?

Diagnosis involves bone marrow biopsy showing lymphoplasmacytic infiltration and MYD88 L265P mutation testing.

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