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Home/Diagnosis/ICD-10 Coding for Thrombocythemia

ICD-10 Coding for Thrombocythemia

D47.3
D75.81

Complete ICD-10-CM coding and documentation guide for icd-10 coding for thrombocythemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Essential thrombocythemia
Primary thrombocytosis
Reactive thrombocytosis
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Key Information: ICD-10 Coding for Thrombocythemia

Essential facts and insights about ICD-10 Coding for Thrombocythemia

Use ICD-10 code D47.3 for essential thrombocythemia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Essential thrombocythemia

Billable Code
D47.3
Billable

Diagnostic Criteria

clinical:
  • • Presence of JAK2 mutation and sustained high platelet count
documentation:
  • • Exclusion of reactive causes documented

Applicable To

  • • Primary thrombocytosis

Important Notes

  • • Ensure documentation includes genetic testing results and exclusion of secondary causes.

Secondary thrombocytosis

Billable Code
D75.81
Billable

Diagnostic Criteria

clinical:
  • • Platelet elevation with identifiable reactive cause
  • • Normal CRP and ESR levels

Applicable To

  • • Reactive thrombocytosis

Important Notes

  • • Ensure the underlying condition is coded first.
Frequently Asked Questions

What is the ICD-10 code for essential thrombocythemia?

The ICD-10 code for essential thrombocythemia is D47.3, used when genetic testing confirms the condition and secondary causes are excluded.

How do you differentiate essential from secondary thrombocytosis?

Essential thrombocytosis is confirmed by genetic mutations (JAK2, CALR, MPL) and sustained high platelet counts, while secondary is due to reactive causes.

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