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Home/Diagnosis/ICD-10 Coding for Thalassemia Anemia

ICD-10 Coding for Thalassemia Anemia

D56.0
D56.1

Complete ICD-10-CM coding and documentation guide for icd-10 coding for thalassemia anemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Cooley's Anemia
Mediterranean Anemia
Hemoglobinopathy
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Key Information: ICD-10 Coding for Thalassemia Anemia

Essential facts and insights about ICD-10 Coding for Thalassemia Anemia

Use ICD-10 code D56.0 for alpha thalassemia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Alpha thalassemia

Billable Code
D56.0
Billable

Diagnostic Criteria

  • • Presence of HbH on electrophoresis

Applicable To

  • • Hemoglobin H disease
  • • Alpha thalassemia major

Important Notes

  • • Ensure genetic testing results are documented to support the use of this code.

Beta thalassemia

Billable Code
D56.1
Billable

Diagnostic Criteria

  • • HPLC showing elevated HbA2
  • • Genetic testing confirming β-globin mutation

Applicable To

  • • Beta thalassemia major
  • • Beta thalassemia intermedia

Important Notes

  • • Document transfusion history and genetic testing results to support coding.
Ancillary Codes

Additional codes that may be used with this diagnosis

Z79.2

Long-term (current) use of other medications

Use when patient is on iron chelation therapy.

Frequently Asked Questions

What is the ICD-10 code for beta thalassemia?

The ICD-10 code for beta thalassemia is D56.1, used for confirmed cases with elevated HbA2 levels.

How is thalassemia anemia documented?

Thalassemia anemia documentation should include type, genetic testing results, and treatment details like transfusion history.

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