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Home/Diagnosis/ICD-10 Coding for Thalassemia

ICD-10 Coding for Thalassemia

D56.1
D56.3

Complete ICD-10-CM coding and documentation guide for icd-10 coding for thalassemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Cooley's Anemia
Mediterranean Anemia
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Key Information: ICD-10 Coding for Thalassemia

Essential facts and insights about ICD-10 Coding for Thalassemia

Use ICD-10 code D56.1 for beta thalassemia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Beta thalassemia

Billable Code
D56.1
Billable

Diagnostic Criteria

  • • Patient requires regular blood transfusions.
  • • Hb <7 g/dL
  • • β⁰/β⁺ mutation
  • • Elevated HbF (>10%)

Applicable To

  • • Beta thalassemia major
  • • Beta thalassemia intermedia

Important Notes

  • • Ensure documentation specifies 'beta thalassemia major' or 'intermedia'.

Thalassemia minor

Billable Code
D56.3
Billable

Diagnostic Criteria

  • • Normal Hb (12-16 g/dL)
  • • MCV <80 fL
  • • β-globin heterozygosity

Applicable To

  • • Beta thalassemia minor

Important Notes

  • • Ensure documentation confirms carrier status.
Ancillary Codes

Additional codes that may be used with this diagnosis

R18.1

Hepatomegaly

Use when hepatomegaly is present as a complication.

Frequently Asked Questions

What is the ICD-10 code for beta thalassemia?

The ICD-10 code for beta thalassemia major and intermedia is D56.1. It is used for patients requiring regular transfusions.

How is thalassemia documented in medical records?

Thalassemia documentation should include genetic test results, transfusion history, and specific Hb levels to ensure accurate coding.

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