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Home/Diagnosis/ICD-10 Coding for Spinal Muscular Atrophy

ICD-10 Coding for Spinal Muscular Atrophy

G12.0
G12.1
G12.9

Complete ICD-10-CM coding and documentation guide for icd-10 coding for spinal muscular atrophy includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
SMA5q
SMAProximal Spinal Muscular Atrophy
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Key Information: ICD-10 Coding for Spinal Muscular Atrophy

Essential facts and insights about ICD-10 Coding for Spinal Muscular Atrophy

Use ICD-10 code G12.0 for infantile spinal muscular atrophy, type i [werdnig-hoffmann], ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Infantile spinal muscular atrophy, type I [Werdnig-Hoffmann]

Billable Code
G12.0
Billable

Diagnostic Criteria

  • • Infantile onset with genetic confirmation

Applicable To

  • • Werdnig-Hoffmann disease

Important Notes

  • • Ensure genetic testing results are documented.

Other inherited spinal muscular atrophy

Billable Code
G12.1
Billable

Diagnostic Criteria

  • • Late-onset SMA with confirmed genetic testing

Applicable To

  • • Kugelberg-Welander disease

Important Notes

  • • Document SMN2 copy number for accurate coding.

Spinal muscular atrophy, unspecified

Billable Code
G12.9
Billable

Diagnostic Criteria

  • • Use only when genetic testing is pending.

Important Notes

  • • Avoid use unless absolutely necessary.
Ancillary Codes

Additional codes that may be used with this diagnosis

J96.9

Respiratory failure, unspecified

Use when documenting respiratory complications in SMA.

M41.9

Scoliosis, unspecified

Use when scoliosis is present in SMA patients.

Frequently Asked Questions

What is the ICD-10 code for spinal muscular atrophy?

The ICD-10 code for spinal muscular atrophy includes G12.0 for infantile type and G12.1 for other inherited forms. Use G12.9 only if genetic testing is pending.

How do you code SMA with respiratory failure?

For SMA with respiratory failure, use G12.1 for the SMA type and J96.9 for respiratory failure. Document genetic confirmation and respiratory assessment.

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