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Home/Diagnosis/ICD-10 Coding for Sickle Cell Pain Crisis

ICD-10 Coding for Sickle Cell Pain Crisis

D57.00
D57.219
D57.40

Complete ICD-10-CM coding and documentation guide for icd-10 coding for sickle cell pain crisis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Vaso-occlusive crisis
Sickle cell crisis
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Key Information: ICD-10 Coding for Sickle Cell Pain Crisis

Essential facts and insights about ICD-10 Coding for Sickle Cell Pain Crisis

Use ICD-10 code D57.00 for sickle-cell anemia without crisis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Sickle-cell anemia without crisis

Billable Code
D57.00
Billable

Diagnostic Criteria

clinical:
  • • Patient is stable with no acute symptoms.

Applicable To

  • • Stable sickle-cell anemia

Important Notes

  • • Ensure no crisis symptoms are present.

Sickle-cell/Hb-C disease with crisis

Billable Code
D57.219
Billable

Diagnostic Criteria

clinical:
  • • Pain score ≥7/10
  • • Elevated lactate dehydrogenase (LDH) >300 U/L
  • • Reticulocytosis >3%

Applicable To

  • • Acute pain crisis in Hb SC disease

Important Notes

  • • Ensure documentation of crisis symptoms and lab findings.

Sickle-cell thalassemia with crisis

Billable Code
D57.40
Billable

Diagnostic Criteria

clinical:
  • • Microcytosis (MCV <80 fL)
  • • Hb electrophoresis confirmation

Applicable To

  • • Crisis in Sβ-thalassemia

Important Notes

  • • Document genotype and crisis symptoms clearly.
Ancillary Codes

Additional codes that may be used with this diagnosis

J96.01

Acute respiratory failure with hypoxia

Use when acute chest syndrome is present.

Frequently Asked Questions

What is the ICD-10 code for sickle cell pain crisis?

The ICD-10 code for sickle cell pain crisis is D57.219 for Hb SC disease with crisis.

How do you document a sickle cell pain crisis?

Document specific triggers, pain severity, and lab results to support coding for a sickle cell pain crisis.

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