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Home/Diagnosis/ICD-10 Coding for Sickle Cell Anemia

ICD-10 Coding for Sickle Cell Anemia

D57.0
D57.1

Complete ICD-10-CM coding and documentation guide for icd-10 coding for sickle cell anemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Sickle Cell Disease
Sickle Cell Disorder
SCD
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Key Information: ICD-10 Coding for Sickle Cell Anemia

Essential facts and insights about ICD-10 Coding for Sickle Cell Anemia

Use ICD-10 code D57.0 for sickle-cell anemia without crisis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Sickle-cell anemia without crisis

Non-Billable
D57.0
Non-Billable

Diagnostic Criteria

  • • Patient has HbSS genotype without acute crisis symptoms.

Applicable To

  • • HbSS without crisis

Important Notes

  • • Ensure crisis symptoms are clearly documented to avoid misclassification.

Sickle-cell anemia with crisis

Billable Code
D57.1
Billable

Diagnostic Criteria

  • • Hemoglobin electrophoresis confirming HbSS
  • • Documentation of acute crisis symptoms such as severe pain or organ dysfunction

Applicable To

  • • HbSS with vaso-occlusive crisis

Important Notes

  • • Ensure crisis and any complications are well-documented.
Ancillary Codes

Additional codes that may be used with this diagnosis

G89.21

Acute pain due to sickle-cell crisis

Use when documenting pain management during a crisis.

J18.9

Acute chest syndrome

Use when acute chest syndrome is present during a crisis.

Frequently Asked Questions

What is the ICD-10 code for sickle cell anemia with crisis?

The ICD-10 code for sickle cell anemia with crisis is D57.1. It is used when a patient is experiencing an acute sickle cell crisis.

How do you code sickle cell anemia without crisis?

For sickle cell anemia without crisis, use ICD-10 code D57.0. Ensure no acute crisis symptoms are present.

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