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Home/Diagnosis/ICD-10 Coding for Primary Myelofibrosis

ICD-10 Coding for Primary Myelofibrosis

D47.4
D75.81

Complete ICD-10-CM coding and documentation guide for icd-10 coding for primary myelofibrosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Chronic Idiopathic Myelofibrosis
Agnogenic Myeloid Metaplasia
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Key Information: ICD-10 Coding for Primary Myelofibrosis

Essential facts and insights about ICD-10 Coding for Primary Myelofibrosis

Use ICD-10 code D47.4 for osteomyelofibrosis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Osteomyelofibrosis

Billable Code
D47.4
Billable

Diagnostic Criteria

clinical:
  • • Presence of JAK2, CALR, or MPL mutations
documentation:
  • • Bone marrow biopsy showing fibrosis grade ≥2
coding:
  • • Exclusion of other myeloid neoplasms

Applicable To

  • • Chronic idiopathic myelofibrosis
  • • Primary myelofibrosis

Important Notes

  • • Ensure documentation specifies 'primary' or 'idiopathic' to use D47.4.

Myelofibrosis

Billable Code
D75.81
Billable

Diagnostic Criteria

clinical:
  • • Documentation of secondary cause or unspecified myelofibrosis

Applicable To

  • • Secondary myelofibrosis NOS

Important Notes

  • • Ensure secondary cause is documented if applicable.
Ancillary Codes

Additional codes that may be used with this diagnosis

R50.9

Fever, unspecified

Use for constitutional symptoms like fever associated with myelofibrosis.

D64.9

Anemia, unspecified

Use when anemia is present and requires transfusion support.

R16.1

Splenomegaly, not elsewhere classified

Use when splenomegaly is confirmed by imaging or physical exam.

Frequently Asked Questions

What is the ICD-10 code for primary myelofibrosis?

The ICD-10 code for primary myelofibrosis is D47.4, which includes chronic idiopathic myelofibrosis.

How do you code secondary myelofibrosis?

Secondary myelofibrosis is coded as D75.81, used when the condition is secondary to another disease or unspecified.

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