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Home/Diagnosis/ICD-10 Coding for Primary Biliary Cirrhosis

ICD-10 Coding for Primary Biliary Cirrhosis

K74.3
K83.0

Complete ICD-10-CM coding and documentation guide for icd-10 coding for primary biliary cirrhosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Primary Biliary Cholangitis
PBC
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Key Information: ICD-10 Coding for Primary Biliary Cirrhosis

Essential facts and insights about ICD-10 Coding for Primary Biliary Cirrhosis

Use ICD-10 code K74.3 for primary biliary cirrhosis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Primary biliary cirrhosis

Billable Code
K74.3
Billable

Diagnostic Criteria

clinical:
  • • Liver biopsy confirms cirrhosis
documentation:
  • • Explicit mention of 'primary biliary cirrhosis'

Applicable To

  • • Primary biliary cholangitis with cirrhosis

Important Notes

  • • Ensure cirrhosis is documented before using K74.3.

Cholangitis, primary

Non-Billable
K83.0
Non-Billable

Diagnostic Criteria

clinical:
  • • AMA positivity
  • • Elevated alkaline phosphatase >1.5x ULN for >6 months

Applicable To

  • • Primary biliary cholangitis without cirrhosis

Important Notes

  • • Ensure cirrhosis is not documented before using K83.0.
Ancillary Codes

Additional codes that may be used with this diagnosis

R18.0

Malignant ascites

Use if ascites is present with PBC-related portal hypertension.

I85.01

Esophageal varices with bleeding

Use for variceal complications.

Frequently Asked Questions

What is the ICD-10 code for primary biliary cirrhosis?

The ICD-10 code for primary biliary cirrhosis is K74.3, used when cirrhosis is confirmed. For primary biliary cholangitis without cirrhosis, use K83.0.

How do you code primary biliary cholangitis without cirrhosis?

Primary biliary cholangitis without cirrhosis is coded as K83.0. Ensure documentation specifies the absence of cirrhosis.

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