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Home/Diagnosis/ICD-10 Coding for Primary Biliary Cholangitis

ICD-10 Coding for Primary Biliary Cholangitis

K83.0
K74.3

Complete ICD-10-CM coding and documentation guide for icd-10 coding for primary biliary cholangitis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Primary Biliary Cirrhosis
Autoimmune Cholangitis
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Key Information: ICD-10 Coding for Primary Biliary Cholangitis

Essential facts and insights about ICD-10 Coding for Primary Biliary Cholangitis

Use ICD-10 code K83.0 for cholangitis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Cholangitis

Non-Billable
K83.0
Non-Billable

Diagnostic Criteria

documentation_criteria:
  • • Absence of cirrhosis in clinical notes.
applicable_to:
  • • Primary biliary cholangitis without cirrhosis
excludes:
  • • Primary biliary cirrhosis with cirrhosis (K74.3)
validation:
  • • AMA positivity
  • • Elevated ALP
  • • Liver biopsy showing florid duct lesions

Important Notes

  • • Ensure documentation specifies absence of cirrhosis.

Primary biliary cirrhosis with cirrhosis

Billable Code
K74.3
Billable

Diagnostic Criteria

applicable_to:
  • • Primary biliary cholangitis with cirrhosis
excludes:
  • • Primary biliary cholangitis without cirrhosis (K83.0)
validation:
  • • Documentation of cirrhosis
  • • Liver biopsy showing cirrhosis

Important Notes

  • • Ensure cirrhosis is clearly documented.
Ancillary Codes

Additional codes that may be used with this diagnosis

R94.5

Abnormal liver function test

Use to document abnormal liver function tests associated with PBC.

R18.0

Ascites

Use to document ascites as a complication of cirrhosis.

Frequently Asked Questions

What is the ICD-10 code for primary biliary cholangitis?

The ICD-10 code for primary biliary cholangitis without cirrhosis is K83.0, while with cirrhosis it is K74.3.

How do you code primary biliary cholangitis with cirrhosis?

Code K74.3 is used for primary biliary cholangitis with documented cirrhosis.

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