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Home/Diagnosis/ICD-10 Coding for Polycythemia Vera

ICD-10 Coding for Polycythemia Vera

D45

Complete ICD-10-CM coding and documentation guide for icd-10 coding for polycythemia vera includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Primary Polycythemia
Vaquez Disease
Vaquez's disease
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Key Information: ICD-10 Coding for Polycythemia Vera

Essential facts and insights about ICD-10 Coding for Polycythemia Vera

Use ICD-10 code D45 for polycythemia vera, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Polycythemia vera

Billable Code
D45
Billable

Diagnostic Criteria

clinical:
  • • Presence of JAK2 mutation and low serum EPO
documentation:
  • • Detailed lab results and bone marrow biopsy findings

Applicable To

  • • Primary polycythemia
  • • Vaquez disease

Important Notes

  • • Ensure documentation includes all WHO criteria for diagnosis.
Ancillary Codes

Additional codes that may be used with this diagnosis

81403

JAK2 exon 12 sequencing

Use for genetic testing to confirm JAK2 mutations.

81404

JAK2 V617F variant analysis

Use for genetic testing to confirm JAK2 mutations.

Z79.891

Long-term use of hydroxyurea

Use when documenting long-term medication management for polycythemia vera.

Frequently Asked Questions

What is the ICD-10 code for polycythemia vera?

The ICD-10 code for polycythemia vera is D45. It is used for diagnosing this myeloproliferative disorder characterized by increased red blood cell mass.

How is polycythemia vera diagnosed?

Polycythemia vera is diagnosed using criteria such as elevated Hgb/HCT levels, JAK2 mutation, and low serum EPO levels. A bone marrow biopsy may also be performed.

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