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Home/Diagnosis/ICD-10 Coding for Polycythemia

ICD-10 Coding for Polycythemia

D45
D75.1

Complete ICD-10-CM coding and documentation guide for icd-10 coding for polycythemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Polycythemia vera
Secondary polycythemia
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Key Information: ICD-10 Coding for Polycythemia

Essential facts and insights about ICD-10 Coding for Polycythemia

Use ICD-10 code D45 for polycythemia vera, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Polycythemia vera

Billable Code
D45
Billable

Diagnostic Criteria

clinical:
  • • JAK2 V617F mutation positive
documentation:
  • • Documented low serum EPO

Applicable To

  • • Primary polycythemia

Important Notes

  • • Ensure JAK2 mutation testing is documented.

Secondary polycythemia

Billable Code
D75.1
Billable

Diagnostic Criteria

clinical:
  • • Elevated EPO
  • • Absence of JAK2 mutation

Applicable To

  • • Polycythemia due to hypoxia
  • • Polycythemia due to renal tumors

Important Notes

  • • Document the underlying cause of secondary polycythemia.
Ancillary Codes

Additional codes that may be used with this diagnosis

D47.1

Chronic myeloproliferative disease

Use if PV evolves into myelofibrosis.

Frequently Asked Questions

What is the ICD-10 code for polycythemia vera?

The ICD-10 code for polycythemia vera is D45. It is used when the condition is confirmed by clinical and laboratory findings, including JAK2 mutation testing.

How is secondary polycythemia coded in ICD-10?

Secondary polycythemia is coded as D75.1 in ICD-10. This code is used when polycythemia is due to underlying conditions like hypoxia or renal tumors.

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