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Home/Diagnosis/ICD-10 Coding for Polycythaemia

ICD-10 Coding for Polycythaemia

D45
D75.0
D75.1

Complete ICD-10-CM coding and documentation guide for icd-10 coding for polycythaemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Polycythemia vera
Secondary polycythemia
Familial erythrocytosis
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Key Information: ICD-10 Coding for Polycythaemia

Essential facts and insights about ICD-10 Coding for Polycythaemia

Use ICD-10 code D45 for polycythemia vera, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Polycythemia vera

Billable Code
D45
Billable

Diagnostic Criteria

clinical:
  • • JAK2 mutation
  • • Elevated hematocrit/hemoglobin
documentation:
  • • Bone marrow biopsy showing trilineage hyperplasia

Applicable To

  • • Primary polycythemia

Important Notes

  • • Ensure documentation includes JAK2 status and bone marrow findings.

Familial erythrocytosis

Billable Code
D75.0
Billable

Diagnostic Criteria

clinical:
  • • EPOR mutation
  • • Normal EPO levels
  • • Family history

Applicable To

  • • Familial polycythemia

Important Notes

  • • Document genetic test results confirming EPOR mutation.

Secondary polycythemia

Billable Code
D75.1
Billable

Diagnostic Criteria

clinical:
  • • History of smoking, COPD, or high-altitude living
  • • Normal or elevated EPO levels

Applicable To

  • • Reactive erythrocytosis

Important Notes

  • • Ensure documentation includes secondary cause like smoking or high-altitude exposure.
Frequently Asked Questions

What is the ICD-10 code for polycythemia vera?

The ICD-10 code for polycythemia vera is D45, used when the condition is confirmed by WHO criteria including JAK2 mutation.

How is secondary polycythemia coded?

Secondary polycythemia is coded as D75.1, applicable when polycythemia results from conditions like smoking or high-altitude living.

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