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Home/Diagnosis/ICD-10 Coding for Osteogenesis Imperfecta Congenita

ICD-10 Coding for Osteogenesis Imperfecta Congenita

Q78.0

Complete ICD-10-CM coding and documentation guide for icd-10 coding for osteogenesis imperfecta congenita includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Brittle Bone Disease
OIC
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Key Information: ICD-10 Coding for Osteogenesis Imperfecta Congenita

Essential facts and insights about ICD-10 Coding for Osteogenesis Imperfecta Congenita

Use ICD-10 code Q78.0 for osteogenesis imperfecta, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Osteogenesis imperfecta

Billable Code
Q78.0
Billable

Diagnostic Criteria

clinical:
  • • Presence of multiple fractures with minimal trauma and blue sclerae
coding:
  • • Use Q78.0 as primary code for all types of osteogenesis imperfecta
documentation:
  • • Document genetic testing results and clinical features

Applicable To

  • • Osteogenesis imperfecta congenita
  • • Osteogenesis imperfecta tarda

Important Notes

  • • Ensure documentation specifies type and associated conditions for accurate coding.
Ancillary Codes

Additional codes that may be used with this diagnosis

M84.5

Pathological fracture in diseases classified elsewhere

Use for coding fractures associated with osteogenesis imperfecta.

H90-H95

Diseases of the ear and mastoid process

Use for coding hearing loss associated with osteogenesis imperfecta.

K00.5

Hereditary disturbances in tooth structure, not elsewhere classified

Use for coding dentinogenesis imperfecta associated with osteogenesis imperfecta.

Frequently Asked Questions

What is the ICD-10 code for osteogenesis imperfecta congenita?

The ICD-10 code for osteogenesis imperfecta congenita is Q78.0, which covers all types of osteogenesis imperfecta.

How is osteogenesis imperfecta congenita diagnosed?

Osteogenesis imperfecta congenita is diagnosed through clinical evaluation, family history, and genetic testing confirming mutations in COL1A1 or COL1A2 genes.

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