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Home/Diagnosis/ICD-10 Coding for Myelofibrosis

ICD-10 Coding for Myelofibrosis

D47.4
D75.81

Complete ICD-10-CM coding and documentation guide for icd-10 coding for myelofibrosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Primary Myelofibrosis
Chronic Idiopathic Myelofibrosis
Post-Polycythemia Vera Myelofibrosis
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Key Information: ICD-10 Coding for Myelofibrosis

Essential facts and insights about ICD-10 Coding for Myelofibrosis

Use ICD-10 code D47.4 for chronic myeloproliferative disease, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Chronic myeloproliferative disease

Billable Code
D47.4
Billable

Diagnostic Criteria

clinical:
  • • Presence of JAK2, CALR, or MPL mutations
documentation:
  • • Bone marrow biopsy results

Applicable To

  • • Chronic idiopathic myelofibrosis
  • • Primary myelofibrosis

Important Notes

  • • Ensure documentation specifies primary versus secondary myelofibrosis.

Other specified diseases of blood and blood-forming organs

Billable Code
D75.81
Billable

Diagnostic Criteria

documentation:
  • • Documentation of underlying condition such as post-PV or post-ET

Applicable To

  • • Secondary myelofibrosis

Important Notes

  • • Ensure the underlying condition is documented and coded first.
Ancillary Codes

Additional codes that may be used with this diagnosis

R16.1

Splenomegaly, not elsewhere classified

Use if splenomegaly is symptomatic.

D63.0

Anemia in neoplastic disease

Use if anemia requires separate treatment.

Frequently Asked Questions

What is the ICD-10 code for primary myelofibrosis?

The ICD-10 code for primary myelofibrosis is D47.4, used for chronic idiopathic myelofibrosis with documented bone marrow findings.

How do you code secondary myelofibrosis?

Secondary myelofibrosis is coded as D75.81, with the underlying condition coded first, such as post-polycythemia vera.

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