DocScrib
How it WorksPricingBlog
Sign InSign UpBook a Demo
DocScrib

AI-powered medical documentation platform streamlining healthcare workflows through intelligent transcription and clinical note generation.

Book a Demo

Product

  • Medical Templates
  • Pricing
  • Integrations
  • Security & Compliance

Resources

  • Blog
  • Documentation
  • Case Studies

Contact

  • support@docscrib.com
  • +1 (555) 123-4567
  • 123 Healthcare Blvd
    Medical District, CA 90210
© 2025 DocScrib. All rights reserved.
Privacy PolicyTerms of ServiceCookie Policy
Home/Diagnosis/ICD-10 Coding for Mastocytosis

ICD-10 Coding for Mastocytosis

D47.02
C96.21
D47.01

Complete ICD-10-CM coding and documentation guide for icd-10 coding for mastocytosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Mast cell disease
Systemic mastocytosis
Cutaneous mastocytosis
Join 10,000+ Happy Clinicians

The AI Medical Scribe for Happiest Clinicians

Save 2+ hours daily with instant clinical documentation.
Our AI scribe listens, understands, and generates comprehensive medical notes so you can focus on patient care.

Start Free Trial
No credit card required•HIPAA compliant
Recording Controls
Start recording to see live transcription
Live Conversation - Try For Free!
Real-time transcription with automatic speaker identification

Ready to Record

Start recording to see live conversation transcription

Key Information: ICD-10 Coding for Mastocytosis

Essential facts and insights about ICD-10 Coding for Mastocytosis

Use ICD-10 code D47.02 for systemic mastocytosis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Systemic mastocytosis

Billable Code
D47.02
Billable

Diagnostic Criteria

clinical:
  • • Presence of multifocal dense mast cell infiltrates in bone marrow
documentation:
  • • Detailed biopsy and genetic test results

Applicable To

  • • Indolent systemic mastocytosis
  • • Smoldering systemic mastocytosis

Important Notes

  • • Ensure documentation specifies systemic involvement and genetic markers.

Aggressive systemic mastocytosis

Billable Code
C96.21
Billable

Diagnostic Criteria

clinical:
  • • Organ damage such as cytopenias or hepatomegaly
  • • C-findings like ascites or hypoalbuminemia

Applicable To

  • • Aggressive mast cell disease

Important Notes

  • • Ensure documentation of aggressive features and organ involvement.

Cutaneous mastocytosis

Billable Code
D47.01
Billable

Diagnostic Criteria

clinical:
  • • Positive Darier’s sign
  • • Skin biopsy with spindle-shaped mast cells

Applicable To

  • • Urticaria pigmentosa

Important Notes

  • • Ensure documentation specifies skin involvement and biopsy results.

Congenital cutaneous mastocytosis

Billable Code
Q82.2
Billable

Diagnostic Criteria

clinical:
  • • Documentation of congenital origin
  • • Presence since birth

Applicable To

  • • Congenital urticaria pigmentosa

Important Notes

  • • Ensure documentation specifies congenital onset.
Ancillary Codes

Additional codes that may be used with this diagnosis

R50.9

Fever, unspecified

Use to document fever associated with systemic mastocytosis.

K90.0

Malabsorption, unspecified

Use for gastrointestinal complications due to mast cell infiltration.

Frequently Asked Questions

What is the ICD-10 code for systemic mastocytosis?

The ICD-10 code for systemic mastocytosis is D47.02, used when systemic involvement is confirmed with bone marrow biopsy and elevated tryptase levels.

How is aggressive systemic mastocytosis coded?

Aggressive systemic mastocytosis is coded as C96.21, used when there is documented organ damage and C-findings.

Quick Navigation
All DiagnosesICD-10 Codes

Related Resources

How Medical Coding WorksBrowse All Codes