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Home/Diagnosis/ICD-10 Coding for Lymphoproliferative Disorder

ICD-10 Coding for Lymphoproliferative Disorder

D47.Z1
D76.1

Complete ICD-10-CM coding and documentation guide for icd-10 coding for lymphoproliferative disorder includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Lymphoproliferative Disease
Lymphoid Proliferative Disorder
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Key Information: ICD-10 Coding for Lymphoproliferative Disorder

Essential facts and insights about ICD-10 Coding for Lymphoproliferative Disorder

Use ICD-10 code D47.Z1 for post-transplant lymphoproliferative disorder, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Post-transplant lymphoproliferative disorder

Billable Code
D47.Z1
Billable

Diagnostic Criteria

clinical:
  • • Biopsy-confirmed lymphoproliferative disorder post-transplant
documentation:
  • • Document EBV status and transplant details

Applicable To

  • • PTLD

Important Notes

  • • Ensure documentation includes transplant and EBV status.

Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

Billable Code
D76.1
Billable

Diagnostic Criteria

clinical:
  • • Double-negative T-cells
  • • FAS mutation

Applicable To

  • • Autoimmune Lymphoproliferative Syndrome (ALPS)

Important Notes

  • • Ensure genetic testing and clinical criteria are documented.
Ancillary Codes

Additional codes that may be used with this diagnosis

B97.2

Epstein-Barr virus as the cause of diseases classified elsewhere

Use to specify EBV involvement in PTLD.

Z94.0

Kidney transplant status

Use to indicate transplant status in PTLD cases.

Frequently Asked Questions

How is lymphoproliferative disorder coded in ICD-10?

Lymphoproliferative disorder post-transplant is coded as D47.Z1, with additional codes for EBV status and transplant details.

What is the ICD-10 code for PTLD?

The ICD-10 code for Post-transplant lymphoproliferative disorder (PTLD) is D47.Z1.

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