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Home/Diagnosis/ICD-10 Coding for Kawasaki Disease

ICD-10 Coding for Kawasaki Disease

M30.3

Complete ICD-10-CM coding and documentation guide for icd-10 coding for kawasaki disease includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Mucocutaneous Lymph Node Syndrome
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Key Information: ICD-10 Coding for Kawasaki Disease

Essential facts and insights about ICD-10 Coding for Kawasaki Disease

Use ICD-10 code M30.3 for mucocutaneous lymph node syndrome [kawasaki], ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Mucocutaneous lymph node syndrome [Kawasaki]

Billable Code
M30.3
Billable

Diagnostic Criteria

clinical_criteria:
  • • Presence of fever for ≥5 days and 4/5 principal clinical features.
documentation_criteria:
  • • Documented echocardiogram findings of coronary artery changes.

Applicable To

  • • Classic Kawasaki disease
  • • Incomplete Kawasaki disease

Important Notes

  • • Ensure all clinical criteria are documented before coding M30.3.
Ancillary Codes

Additional codes that may be used with this diagnosis

I25.41

Coronary artery aneurysm

Use when echocardiogram shows coronary artery aneurysm.

R50.9

Prolonged fever

Use for fever lasting ≥5 days as a symptom of Kawasaki disease.

Frequently Asked Questions

What is the ICD-10 code for Kawasaki disease?

The ICD-10 code for Kawasaki disease is M30.3, used for confirmed cases meeting diagnostic criteria.

How is Kawasaki disease documented?

Document Kawasaki disease with fever duration, principal clinical features, lab results, and echocardiogram findings.

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