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Home/Diagnosis/ICD-10 Coding for Hypogammaglobulinemia

ICD-10 Coding for Hypogammaglobulinemia

D80.0
D80.1
D80.7

Complete ICD-10-CM coding and documentation guide for icd-10 coding for hypogammaglobulinemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Immunoglobulin deficiency
Low immunoglobulin levels
Low gamma globulin levels
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Key Information: ICD-10 Coding for Hypogammaglobulinemia

Essential facts and insights about ICD-10 Coding for Hypogammaglobulinemia

Use ICD-10 code D80.0 for hereditary hypogammaglobulinemia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Hereditary hypogammaglobulinemia

Billable Code
D80.0
Billable

Diagnostic Criteria

  • • Family history of immunodeficiency
  • • Genetic testing confirming specific mutations
  • • IgG levels < 200 mg/dL
  • • Absent B-cells

Applicable To

  • • X-linked agammaglobulinemia
  • • Autosomal recessive agammaglobulinemia

Important Notes

  • • Ensure genetic confirmation is documented.

Nonfamilial hypogammaglobulinemia

Billable Code
D80.1
Billable

Diagnostic Criteria

  • • IgG levels < 400 mg/dL
  • • Recurrent infections
  • • Normal B-cell count

Applicable To

  • • Common variable immunodeficiency (CVID)

Important Notes

  • • Document recurrent infections and IgG levels.

Transient hypogammaglobulinemia of infancy

Billable Code
D80.7
Billable

Diagnostic Criteria

  • • IgG levels < 300 mg/dL in infants
  • • Normalization of IgG by age 3

Applicable To

  • • Temporary immunoglobulin deficiency in infants

Important Notes

  • • Ensure documentation of IgG normalization.
Ancillary Codes

Additional codes that may be used with this diagnosis

J18.9

Pneumonia, unspecified organism

Use to document infections related to hypogammaglobulinemia.

J01.90

Acute sinusitis, unspecified

Document sinusitis as a complication.

Z00.129

Encounter for routine child health examination without abnormal findings

Use for well-child visits in infants with transient hypogammaglobulinemia.

Frequently Asked Questions

What is the ICD-10 code for hereditary hypogammaglobulinemia?

The ICD-10 code for hereditary hypogammaglobulinemia is D80.0, used when genetic testing confirms a hereditary form.

How is nonfamilial hypogammaglobulinemia coded?

Nonfamilial hypogammaglobulinemia is coded as D80.1, applicable when IgG levels are low without a family history.

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