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Home/Diagnosis/ICD-10 Coding for Hyperammonemia

ICD-10 Coding for Hyperammonemia

E72.4
P74.6
K76.82

Complete ICD-10-CM coding and documentation guide for icd-10 coding for hyperammonemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Ammonia Toxicity
Elevated Ammonia Levels
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Key Information: ICD-10 Coding for Hyperammonemia

Essential facts and insights about ICD-10 Coding for Hyperammonemia

Use ICD-10 code E72.4 for disorders of ornithine metabolism, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Disorders of ornithine metabolism

Billable Code
E72.4
Billable

Diagnostic Criteria

  • • Confirmed genetic defect in ornithine metabolism

Applicable To

  • • HHH syndrome

Important Notes

  • • Ensure genetic testing is documented for accurate coding.

Transitory hyperammonemia of newborn

Billable Code
P74.6
Billable

Diagnostic Criteria

  • • Neonatal onset with ammonia >80 µmol/L

Important Notes

  • • Ensure documentation specifies neonatal onset and resolution.

Hepatic encephalopathy

Billable Code
K76.82
Billable

Diagnostic Criteria

  • • Liver disease with altered mental status and elevated ammonia

Important Notes

  • • Do not code hyperammonemia separately unless specified.
Ancillary Codes

Additional codes that may be used with this diagnosis

K76.82

Hepatic encephalopathy

Use when hyperammonemia is due to liver disease.

Frequently Asked Questions

What is the ICD-10 code for hyperammonemia?

The ICD-10 code for hyperammonemia depends on the underlying cause. E72.4 is used for disorders of ornithine metabolism, while P74.6 is for transitory hyperammonemia of newborn.

How is hyperammonemia documented?

Hyperammonemia documentation should include ammonia levels, underlying cause, and any genetic test results confirming urea cycle disorders.

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