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Home/Diagnosis/ICD-10 Coding for Hereditary Hemorrhagic Telangiectasia

ICD-10 Coding for Hereditary Hemorrhagic Telangiectasia

I78.0

Complete ICD-10-CM coding and documentation guide for icd-10 coding for hereditary hemorrhagic telangiectasia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Osler-Weber-Rendu Syndrome
HHT
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Key Information: ICD-10 Coding for Hereditary Hemorrhagic Telangiectasia

Essential facts and insights about ICD-10 Coding for Hereditary Hemorrhagic Telangiectasia

Use ICD-10 code I78.0 for hereditary hemorrhagic telangiectasia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Hereditary hemorrhagic telangiectasia

Billable Code
I78.0
Billable

Diagnostic Criteria

  • • Patient meets Curaçao criteria or has genetic confirmation.

Applicable To

  • • Osler-Weber-Rendu disease

Important Notes

  • • Ensure documentation supports the use of I78.0 by including clinical criteria or genetic test results.
Ancillary Codes

Additional codes that may be used with this diagnosis

I28.0

Pulmonary arteriovenous malformation

Use when imaging confirms a pulmonary AVM.

Frequently Asked Questions

What is the ICD-10 code for hereditary hemorrhagic telangiectasia?

The ICD-10 code for hereditary hemorrhagic telangiectasia is I78.0. It is used when the patient meets clinical criteria or has confirmed genetic mutations.

How is hereditary hemorrhagic telangiectasia diagnosed?

Diagnosis of hereditary hemorrhagic telangiectasia involves meeting Curaçao criteria or confirming genetic mutations through testing.

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