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Home/Diagnosis/ICD-10 Coding for Hemophilia

ICD-10 Coding for Hemophilia

D66
D67

Complete ICD-10-CM coding and documentation guide for icd-10 coding for hemophilia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Hereditary Factor VIII Deficiency
Hereditary Factor IX Deficiency
Bleeding Disorder
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Key Information: ICD-10 Coding for Hemophilia

Essential facts and insights about ICD-10 Coding for Hemophilia

Use ICD-10 code D66 for hereditary factor viii deficiency, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Hereditary factor VIII deficiency

Billable Code
D66
Billable

Diagnostic Criteria

clinical:
  • • Factor VIII activity <40% confirmed by lab tests
documentation:
  • • Family history or genetic testing confirming hereditary status

Applicable To

  • • Hemophilia A

Important Notes

  • • Ensure documentation specifies hereditary status and includes lab results.

Hereditary factor IX deficiency

Billable Code
D67
Billable

Diagnostic Criteria

clinical:
  • • Factor IX activity <40%
  • • Absence of acquired inhibitors

Applicable To

  • • Hemophilia B

Important Notes

  • • Ensure documentation specifies hereditary status and includes lab results.
Ancillary Codes

Additional codes that may be used with this diagnosis

Z14.02

Symptomatic hemophilia A carrier status

Use when documenting symptomatic carrier status in females.

Frequently Asked Questions

What is the ICD-10 code for hemophilia A?

The ICD-10 code for hemophilia A is D66, which represents hereditary factor VIII deficiency.

How do you code acquired hemophilia?

Acquired hemophilia is coded as D68.311, indicating the presence of factor VIII inhibitors.

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