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Home/Diagnosis/ICD-10 Coding for Focal Segmental Glomerulosclerosis

ICD-10 Coding for Focal Segmental Glomerulosclerosis

N04.1

Complete ICD-10-CM coding and documentation guide for icd-10 coding for focal segmental glomerulosclerosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
FSGS
Focal Glomerulosclerosis
focal segmental glomerular lesions
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Key Information: ICD-10 Coding for Focal Segmental Glomerulosclerosis

Essential facts and insights about ICD-10 Coding for Focal Segmental Glomerulosclerosis

Use ICD-10 code N04.1 for nephrotic syndrome with focal and segmental glomerular lesions, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Nephrotic syndrome with focal and segmental glomerular lesions

Billable Code
N04.1
Billable

Diagnostic Criteria

clinical:
  • • Biopsy shows segmental sclerosis and podocyte effacement.
documentation:
  • • Documentation must specify absence of secondary causes.

Applicable To

  • • Biopsy-confirmed FSGS lesions
  • • Nephrotic syndrome with proteinuria ≥3.5 g/day

Important Notes

  • • Ensure documentation specifies primary vs. secondary FSGS.
Ancillary Codes

Additional codes that may be used with this diagnosis

E11.22

Type 2 diabetes with diabetic chronic kidney disease

Use if FSGS is secondary to diabetes.

Z14.8

Genetic susceptibility to renal disease

Use for familial/genetic FSGS.

Frequently Asked Questions

What is the ICD-10 code for FSGS?

The ICD-10 code for Focal Segmental Glomerulosclerosis (FSGS) is N04.1, used for nephrotic syndrome with focal and segmental glomerular lesions.

How do you code FSGS with diabetes?

For FSGS secondary to diabetes, use E11.22 for Type 2 diabetes with chronic kidney disease, followed by N04.1.

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