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Home/Diagnosis/ICD-10 Coding for Essential Thrombocytosis

ICD-10 Coding for Essential Thrombocytosis

D47.3
D75.838

Complete ICD-10-CM coding and documentation guide for icd-10 coding for essential thrombocytosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Essential Thrombocythemia
Primary Thrombocythemia
Idiopathic Thrombocythemia
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Key Information: ICD-10 Coding for Essential Thrombocytosis

Essential facts and insights about ICD-10 Coding for Essential Thrombocytosis

Use ICD-10 code D47.3 for essential (hemorrhagic) thrombocythemia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Essential (hemorrhagic) thrombocythemia

Billable Code
D47.3
Billable

Diagnostic Criteria

clinical:
  • • Presence of JAK2, CALR, or MPL mutations
documentation:
  • • Explicit mention of 'essential' or 'primary' thrombocythemia

Applicable To

  • • Primary thrombocythemia
  • • Idiopathic thrombocythemia

Important Notes

  • • Ensure documentation specifies 'essential' or 'primary' to use D47.3.

Other specified thrombocytosis

Billable Code
D75.838
Billable

Diagnostic Criteria

clinical_validation_requirements:
  • • Documentation of underlying cause
  • • Transient platelet elevation

Applicable To

  • • Reactive thrombocytosis

Important Notes

  • • Ensure linkage to the secondary cause is documented.
Ancillary Codes

Additional codes that may be used with this diagnosis

Z85.6

Personal history of leukemia

Use if there is a history of leukemia progression from essential thrombocythemia.

Frequently Asked Questions

What is the ICD-10 code for essential thrombocytosis?

The ICD-10 code for essential thrombocytosis is D47.3, used when the condition is confirmed by genetic testing and clinical criteria.

How do you differentiate essential thrombocytosis from reactive thrombocytosis?

Essential thrombocytosis is a primary clonal disorder confirmed by genetic markers, while reactive thrombocytosis is secondary to another condition like infection.

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