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Home/Diagnosis/ICD-10 Coding for Dermatomyositis

ICD-10 Coding for Dermatomyositis

M33.12
M33.13
M36.0

Complete ICD-10-CM coding and documentation guide for icd-10 coding for dermatomyositis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
DM
Idiopathic Inflammatory Myopathy
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Key Information: ICD-10 Coding for Dermatomyositis

Essential facts and insights about ICD-10 Coding for Dermatomyositis

Use ICD-10 code M33.12 for other dermatomyositis with myopathy, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Other dermatomyositis with myopathy

Billable Code
M33.12
Billable

Diagnostic Criteria

  • • Proximal muscle weakness (MMT grade ≤4/5)
  • • CK >1,000 IU/L
  • • EMG/myopathy on biopsy

Applicable To

  • • Dermatomyositis with muscle weakness

Important Notes

  • • Ensure documentation of muscle involvement to avoid misclassification.

Other dermatomyositis without myopathy

Billable Code
M33.13
Billable

Diagnostic Criteria

  • • Heliotrope rash/Gottron papules without objective weakness
  • • Normal CK/EMG

Applicable To

  • • Amyopathic dermatomyositis

Important Notes

  • • Ensure absence of myopathy is documented to support this code.

Dermatomyositis in neoplastic disease

Billable Code
M36.0
Billable

Diagnostic Criteria

  • • Dermatomyositis secondary to a specific malignancy
  • • Positive anti-TIF1γ antibody

Applicable To

  • • Paraneoplastic dermatomyositis

Important Notes

  • • Always sequence the malignancy code before M36.0.
Ancillary Codes

Additional codes that may be used with this diagnosis

J84.1

Interstitial lung disease

Use if ILD is present in conjunction with dermatomyositis.

Frequently Asked Questions

What is the ICD-10 code for dermatomyositis with myopathy?

The ICD-10 code for dermatomyositis with myopathy is M33.12. It is used when dermatomyositis is confirmed with muscle involvement.

How do you code dermatomyositis associated with cancer?

For dermatomyositis associated with cancer, use M36.0 and sequence the malignancy code first.

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