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Home/Diagnosis/ICD-10 Coding for Cystic Fibrosis

ICD-10 Coding for Cystic Fibrosis

E84.0
E84.19

Complete ICD-10-CM coding and documentation guide for icd-10 coding for cystic fibrosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
CF
Mucoviscidosis
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Key Information: ICD-10 Coding for Cystic Fibrosis

Essential facts and insights about ICD-10 Coding for Cystic Fibrosis

Use ICD-10 code E84.0 for cystic fibrosis with pulmonary manifestations, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Cystic fibrosis with pulmonary manifestations

Billable Code
E84.0
Billable

Diagnostic Criteria

  • • Presence of chronic cough and sputum production with confirmed CF diagnosis.

Applicable To

  • • Chronic lung disease due to cystic fibrosis

Important Notes

  • • Ensure to document specific pulmonary manifestations and any identified organisms.

Cystic fibrosis with other intestinal manifestations

Billable Code
E84.19
Billable

Diagnostic Criteria

    Applicable To

    • • Meconium ileus
    • • Pancreatic insufficiency

    Important Notes

    • • Document specific intestinal manifestations and any complications.
    Ancillary Codes

    Additional codes that may be used with this diagnosis

    B96.5

    Pseudomonas (aeruginosa) as the cause of diseases classified elsewhere

    Use when Pseudomonas is identified in cultures.

    Frequently Asked Questions

    What is the ICD-10 code for cystic fibrosis with pulmonary manifestations?

    The ICD-10 code for cystic fibrosis with pulmonary manifestations is E84.0. It is used when the patient presents with symptoms such as chronic cough and bronchiectasis.

    How do you code cystic fibrosis with intestinal manifestations?

    Use ICD-10 code E84.19 for cystic fibrosis with intestinal manifestations, such as steatorrhea or pancreatic insufficiency.

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