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Home/Diagnosis/ICD-10 Coding for Congenital Heart Disease

ICD-10 Coding for Congenital Heart Disease

Q21.2
Q23.4

Complete ICD-10-CM coding and documentation guide for icd-10 coding for congenital heart disease includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
CHD
Congenital Cardiac Anomaly
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Key Information: ICD-10 Coding for Congenital Heart Disease

Essential facts and insights about ICD-10 Coding for Congenital Heart Disease

Use ICD-10 code Q21.2 for atrioventricular septal defect, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Atrioventricular septal defect

Non-Billable
Q21.2
Non-Billable

Diagnostic Criteria

  • • Echocardiogram confirms common atrioventricular valve.

Applicable To

  • • Endocardial cushion defect
  • • Ostium primum defect

Important Notes

  • • Ensure echocardiogram confirms the defect type.

Hypoplastic left heart syndrome

Billable Code
Q23.4
Billable

Diagnostic Criteria

  • • Echocardiogram confirms HLHS.

Applicable To

  • • Underdeveloped left ventricle
  • • Aortic atresia

Important Notes

  • • Confirm with detailed imaging reports.
Ancillary Codes

Additional codes that may be used with this diagnosis

I27.0

Pulmonary hypertension

Use when pulmonary hypertension is secondary to AVSD.

I42.0

Dilated cardiomyopathy

Use if cardiomyopathy is present with HLHS.

Frequently Asked Questions

What is the ICD-10 code for congenital heart disease?

The ICD-10 code for congenital heart disease varies by specific defect, such as Q21.2 for atrioventricular septal defect or Q23.4 for hypoplastic left heart syndrome.

When should Q24.9 be used?

Use Q24.9 only when specific details of the congenital heart defect are unavailable and no echocardiogram or surgical reports are present.

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