Complete ICD-10-CM coding and documentation guide for icd-10 coding for congenital adrenal hyperplasia includes clinical validation requirements, medical necessity guidelines, and coding policies.
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Essential facts and insights about ICD-10 Coding for Congenital Adrenal Hyperplasia
Use ICD-10 code E25.0 for congenital adrenogenital disorders associated with enzyme deficiency, ensuring proper documentation in clinical notes.
Additional codes that may be used with this diagnosis
Addisonian crisis
Use for acute adrenal insufficiency related to CAH.
Hypokalemia
Use for electrolyte imbalances in salt-wasting CAH.
The ICD-10 code for congenital adrenal hyperplasia due to 21-hydroxylase deficiency is E25.0. This code is used when enzyme deficiency is confirmed.
Documentation for congenital adrenal hyperplasia should include specific enzyme deficiency, lab results like elevated 17-OHP, and genetic testing results.