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Home/Diagnosis/ICD-10 Coding for Chronic Interstitial Lung Disease

ICD-10 Coding for Chronic Interstitial Lung Disease

J84.112
J84.89
J84.10

Complete ICD-10-CM coding and documentation guide for icd-10 coding for chronic interstitial lung disease includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Chronic ILD
Pulmonary Fibrosis
Interstitial Pulmonary Disease
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Key Information: ICD-10 Coding for Chronic Interstitial Lung Disease

Essential facts and insights about ICD-10 Coding for Chronic Interstitial Lung Disease

Use ICD-10 code J84.112 for idiopathic pulmonary fibrosis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Idiopathic pulmonary fibrosis

Billable Code
J84.112
Billable

Diagnostic Criteria

clinical:
  • • HRCT shows honeycombing and traction bronchiectasis.
documentation:
  • • Multidisciplinary discussion confirms diagnosis.

Applicable To

  • • Usual interstitial pneumonia

Important Notes

  • • Ensure documentation includes HRCT findings and multidisciplinary discussion notes.

Other specified interstitial pulmonary diseases

Billable Code
J84.89
Billable

Diagnostic Criteria

clinical:
  • • Specific connective tissue disease diagnosis
  • • Radiologic correlation with CTD

Applicable To

  • • Interstitial lung disease associated with connective tissue disease

Important Notes

  • • Ensure the underlying connective tissue disease is documented and coded.

Pulmonary fibrosis, unspecified

Billable Code
J84.10
Billable

Diagnostic Criteria

clinical:
  • • Exclusion of known causes after full workup

Applicable To

  • • Unclassifiable fibrosis

Important Notes

  • • Use only after thorough exclusion of other causes.
Ancillary Codes

Additional codes that may be used with this diagnosis

I27.21

Secondary pulmonary hypertension

Use when pulmonary hypertension is secondary to ILD.

M05.1-

Rheumatoid lung disease

Use when ILD is due to rheumatoid arthritis.

Frequently Asked Questions

What is the ICD-10 code for idiopathic pulmonary fibrosis?

The ICD-10 code for idiopathic pulmonary fibrosis is J84.112. It requires confirmation by HRCT and a multidisciplinary discussion.

How do you code interstitial lung disease associated with rheumatoid arthritis?

Code M05.11 for rheumatoid arthritis with lung involvement, followed by J84.89 for the interstitial lung disease.

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