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Home/Diagnosis/ICD-10 Coding for Charcot-Marie-Tooth Disease

ICD-10 Coding for Charcot-Marie-Tooth Disease

G60.0

Complete ICD-10-CM coding and documentation guide for icd-10 coding for charcot-marie-tooth disease includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
CMT
Hereditary Motor and Sensory Neuropathy
Peroneal Muscular Atrophy
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Key Information: ICD-10 Coding for Charcot-Marie-Tooth Disease

Essential facts and insights about ICD-10 Coding for Charcot-Marie-Tooth Disease

Use ICD-10 code G60.0 for hereditary motor and sensory neuropathy, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Hereditary motor and sensory neuropathy

Billable Code
G60.0
Billable

Diagnostic Criteria

clinical:
  • • Genetic testing confirms PMP22 duplication or MFN2 mutation.
documentation:
  • • Detailed clinical documentation of symptoms and genetic test results.

Applicable To

  • • Charcot-Marie-Tooth disease
  • • Peroneal muscular atrophy
  • • Déjérine-Sottas disease

Important Notes

  • • Ensure genetic and clinical confirmation of CMT before coding.
  • • Avoid using unspecified codes when specific diagnosis is available.
Ancillary Codes

Additional codes that may be used with this diagnosis

M21.6X-

Other acquired deformities of limbs

Use for documenting pes cavus deformity associated with CMT.

R26.2

Difficulty in walking, not elsewhere classified

Use for documenting gait abnormalities such as foot drop.

M62.81

Muscle weakness (generalized)

Use for documenting muscle weakness related to CMT.

Z84.89

Family history of other specified conditions

Use for documenting family history of hereditary neuropathies.

Frequently Asked Questions

What is the ICD-10 code for Charcot-Marie-Tooth disease?

The ICD-10 code for Charcot-Marie-Tooth disease is G60.0, which covers hereditary motor and sensory neuropathy.

How is Charcot-Marie-Tooth disease diagnosed?

Charcot-Marie-Tooth disease is diagnosed through genetic testing confirming mutations like PMP22 duplication, and clinical exams showing muscle weakness and foot deformities.

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