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Home/Diagnosis/ICD-10 Coding for Cardiac Amyloidosis

ICD-10 Coding for Cardiac Amyloidosis

E85.4
I43

Complete ICD-10-CM coding and documentation guide for icd-10 coding for cardiac amyloidosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Amyloid Cardiomyopathy
ATTR-CM
AL Amyloidosis with Cardiac Involvement
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Key Information: ICD-10 Coding for Cardiac Amyloidosis

Essential facts and insights about ICD-10 Coding for Cardiac Amyloidosis

Use ICD-10 code E85.4 for organ-limited amyloidosis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Organ-limited amyloidosis

Billable Code
E85.4
Billable

Diagnostic Criteria

clinical:
  • • Confirmed cardiac involvement with amyloidosis
documentation:
  • • Detailed imaging and lab results confirming amyloidosis type

Applicable To

  • • Cardiac amyloidosis
  • • Amyloid cardiomyopathy

Important Notes

  • • Ensure documentation specifies the type of amyloidosis and its cardiac involvement.

Cardiomyopathy in diseases classified elsewhere

Billable Code
I43
Billable

Diagnostic Criteria

clinical:
  • • Echocardiographic evidence of restrictive cardiomyopathy
  • • CMR findings consistent with amyloidosis

Applicable To

  • • Cardiomyopathy due to amyloidosis

Important Notes

  • • Ensure proper sequencing with E85.4 as the primary code.
Ancillary Codes

Additional codes that may be used with this diagnosis

Z94.1

Heart transplant status

Use when the patient has undergone a heart transplant due to amyloidosis.

I50.3-

Diastolic heart failure

Use when heart failure with preserved ejection fraction is present.

Frequently Asked Questions

What is the ICD-10 code for cardiac amyloidosis?

The ICD-10 code for cardiac amyloidosis is E85.4 for organ-limited amyloidosis, used with I43 for cardiomyopathy.

How do you code cardiac amyloidosis?

Code cardiac amyloidosis with E85.4 for organ-limited amyloidosis and I43 for cardiomyopathy involvement.

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