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Home/Diagnosis/ICD-10 Coding for Beta Thalassemia

ICD-10 Coding for Beta Thalassemia

D56.1
D57.4

Complete ICD-10-CM coding and documentation guide for icd-10 coding for beta thalassemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
B Thalassemia
Thalassemia Major
Thalassemia Intermedia
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Key Information: ICD-10 Coding for Beta Thalassemia

Essential facts and insights about ICD-10 Coding for Beta Thalassemia

Use ICD-10 code D56.1 for beta thalassemia, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Beta thalassemia

Billable Code
D56.1
Billable

Diagnostic Criteria

clinical:
  • • Presence of microcytic anemia with elevated HbA2 and HbF levels.
documentation:
  • • Genetic test results confirming HBB mutations.

Applicable To

  • • Beta thalassemia major
  • • Beta thalassemia intermedia

Important Notes

  • • Ensure genetic confirmation is documented to support the use of D56.1.

Sickle-cell thalassemia

Non-Billable
D57.4
Non-Billable

Diagnostic Criteria

clinical_validation_requirements:
  • • Presence of HbS and beta thalassemia mutation.

Important Notes

  • • Ensure HbS presence is documented.
Ancillary Codes

Additional codes that may be used with this diagnosis

E83.11

Hemochromatosis due to repeated transfusions

Use when iron overload is present due to transfusions.

Frequently Asked Questions

What is the ICD-10 code for beta thalassemia?

The ICD-10 code for beta thalassemia is D56.1, which covers both beta thalassemia major and intermedia.

How is beta thalassemia diagnosed?

Beta thalassemia is diagnosed through blood tests showing microcytic anemia and genetic testing confirming HBB mutations.

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