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Home/Diagnosis/ICD-10 Coding for Amyloidosis

ICD-10 Coding for Amyloidosis

E85.81
E85.82

Complete ICD-10-CM coding and documentation guide for icd-10 coding for amyloidosis includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Amyloid disease
Amyloid protein deposition
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Key Information: ICD-10 Coding for Amyloidosis

Essential facts and insights about ICD-10 Coding for Amyloidosis

Use ICD-10 code E85.81 for al amyloidosis, ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

AL amyloidosis

Billable Code
E85.81
Billable

Diagnostic Criteria

  • • Confirmed AL amyloidosis with organ involvement.

Applicable To

  • • Primary systemic amyloidosis

Important Notes

  • • Ensure organ involvement is documented to support coding.

Hereditary ATTR amyloidosis

Billable Code
E85.82
Billable

Diagnostic Criteria

  • • Use for confirmed ATTR amyloidosis with genetic testing.

Applicable To

  • • Familial amyloid polyneuropathy

Important Notes

  • • Document genetic testing results to support coding.
Ancillary Codes

Additional codes that may be used with this diagnosis

I43

Cardiomyopathy in amyloidosis

Use to specify cardiac involvement in amyloidosis.

G60.8

Other hereditary and idiopathic neuropathies

Use to specify neuropathy involvement in amyloidosis.

Frequently Asked Questions

What is the ICD-10 code for AL amyloidosis?

The ICD-10 code for AL amyloidosis is E85.81, used when light chain amyloidosis is confirmed with organ involvement.

How do you code hereditary ATTR amyloidosis?

Hereditary ATTR amyloidosis is coded as E85.82, requiring confirmation through genetic testing and documentation of organ involvement.

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