Complete ICD-10-CM coding and documentation guide for icd-10 coding for alport syndrome includes clinical validation requirements, medical necessity guidelines, and coding policies.
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Essential facts and insights about ICD-10 Coding for Alport Syndrome
Use ICD-10 code Q87.81 for alport syndrome, ensuring proper documentation in clinical notes.
Additional codes that may be used with this diagnosis
Nephrotic syndrome with proteinuria >3.5g/day
Use for documenting nephrotic syndrome with proteinuria >3.5g/day.
Sensorineural hearing loss
Use when hearing loss is documented with audiometry results.
Anterior lenticonus
Use for ocular manifestations confirmed by ophthalmology exam.
The ICD-10 code for Alport syndrome is Q87.81, used when the diagnosis is confirmed through genetic testing or clinical criteria.
Alport syndrome is diagnosed through genetic testing for COL4A3, COL4A4, or COL4A5 mutations, along with clinical criteria such as hematuria and hearing loss.