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Home/Diagnosis/ICD-10 Coding for Acute Leukemia

ICD-10 Coding for Acute Leukemia

C91.0
C92.0

Complete ICD-10-CM coding and documentation guide for icd-10 coding for acute leukemia includes clinical validation requirements, medical necessity guidelines, and coding policies.

Also Known as:
Acute Lymphoblastic Leukemia
Acute Myeloblastic Leukemia
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Key Information: ICD-10 Coding for Acute Leukemia

Essential facts and insights about ICD-10 Coding for Acute Leukemia

Use ICD-10 code C91.0 for acute lymphoblastic leukemia [all], ensuring proper documentation in clinical notes.

Primary ICD-10-CM Codes

Acute lymphoblastic leukemia [ALL]

Non-Billable
C91.0
Non-Billable

Diagnostic Criteria

  • • Presence of ≥20% lymphoblasts in marrow

Applicable To

  • • T-cell precursor leukemia
  • • B-cell precursor leukemia

Important Notes

  • • Ensure lineage and remission status are documented.

Acute myeloblastic leukemia [AML]

Non-Billable
C92.0
Non-Billable

Diagnostic Criteria

  • • Auer rods on smear
  • • MPO+ staining
  • • NPM1 or CEBPA mutation

Applicable To

  • • M0-M7 FAB classifications

Important Notes

  • • Document genetic markers and FAB classification.
Ancillary Codes

Additional codes that may be used with this diagnosis

D61.818

Pancytopenia

Use if pancytopenia is present with leukemia.

D65

Disseminated intravascular coagulation (DIC)

Use if DIC is present with APL.

Frequently Asked Questions

What is the ICD-10 code for acute leukemia?

The ICD-10 code for acute lymphoblastic leukemia is C91.0, and for acute myeloblastic leukemia, it is C92.0.

How do you code acute leukemia in remission?

For acute lymphoblastic leukemia in remission, use C91.01. For acute myeloblastic leukemia in remission, use C92.01.

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